ACONSELHAMENTO NUTRICIONAL EM PACIENTES PORTADORES DE FIBROSE CÍSTICA: UMA REVISÃO INTEGRATIVA DE LITERATURA

• DOI: 10.22533/at.ed.51520031214

• Palavras-chave: Fibrose cística. Nutrição. Avaliação nutricional.

• Keywords: Cystic fibrosis. Nutrition. Nutritional assessment.

• Abstract:

  Cystic Fibrosis or mucoviscidosis is an autosomal non-transmissible disease
  caused by a defective gene that most commonly affects children. Its clinical
  manifestations result in accumulation of secretions in the lungs, pancreas and
  the digestive system. The aim of the article was to review and analyze the
  impact that nutritional support can have on the improvement of nutritional
  status in patients with cystic fibrosis. This is an integrative literature
  review carried out in the Medical Literature Analysis and Retrieval Sistem
  On-line (MEDLINE / PUBMED), in Latin American and Caribbean Literature (LILACS)
  and in the Scientific Electronic Library Online (SciELO), in Portuguese. and
  English between the years 2012-2020. At the end of the analysis, only 9 studies
  fulfilled the requirements regarding the listed theme, thus the rest were
  discarded. They used the terms: Cystic fibrosis. Nutrition. According to the findings in the studies, it is observed that this pathology is often linked to the status of malnutrition, malnutrition, inflammation, in addition to impairments in the digestion and absorption of nutrients, especially fats, making early monitoring necessary for an intervention. Of success. Therefore, it is concluded that nutritional therapy and long-term follow-up is essential in patients with cystic fibrosis, since this pathology is of a hypercatabolic and inflammatory order that contributes to increased morbidity and mortality. Descriptors: Cystic fibrosis. Nutrition. Nutritional assessment.

  Cystic Fibrosis or mucoviscidosis is a non-transmissible autosomal genetic disease with a prevalence in white people whose clinical manifestations result from protein dysfunction. In recent years the prognosis has improved greatly, showing a positive survivor balance. Thus, the present study aimed to evaluate the effects of dietary intervention in patients with cystic fibrosis disease. The study was a case study, descriptive, exploratory, with a qualitative approach. The subjects of the case study were children of both genders between 4 and 6 years of age, all of whom were diagnosed with cystic fibrosis in August 2014. The main results were the physical state, body mass index (BMI) (P / I), showing that the children were adequate as recommended by the WHO (2006), even so we can realize how difficult it is for the carriers to have a weight gain even with a hypocaloric diet. The study allowed us to see that diet has a direct positive and negative influence on cystic fibrosis (CF).Being visible the lack of professionals with specific knowledge about pathology, including nutritionists. 

• Número de páginas: 12